OMOP Concept 4219277

Mucopolysaccharidosis, MPS-IV-A

StandardConditionSNOMED7259005Disorder
Maps from
2
Descendants
0
Valid from
31 Jan 2002
Valid to
31 Dec 2099
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Source codes that map to this concept

2 source codes normalize to Mucopolysaccharidosis, MPS-IV-A via the OMOP "Maps to" relationship.

VocabularyCodeNameType
CIEL133808Mucopolysaccharidosis, MPS-IV-ANon-standard
ICD10CME76.210Morquio A mucopolysaccharidosesNon-standard

Synonyms

Alternative names recorded for Mucopolysaccharidosis, MPS-IV-A across source vocabularies.

  • Galactosamine-6-sulfatase deficiency
  • Galactosamine-6-sulphatase deficiency
  • Galactose-6-sulfatase deficiency
  • Galactose-6-sulphatase deficiency
  • Morquio A syndrome
  • Morquio's syndrome, classic form
  • Morquio syndrome A
  • MPS IV-A-Mucopolysaccharidosis IV-A
  • mucopolisacaridosis, MPS - IV - A
  • mucopolisacaridosis, MPS - IV - A (trastorno)
  • Mucopolysaccharidosis IV-A
  • Mucopolysaccharidosis IV-A (disorder)
  • N-acetylgalactosamine-6-sulfatase deficiency
  • N-acetylgalactosamine-6-sulphatase deficiency
  • síndrome de Morquio A
  • síndrome de Morquio, forma clásica

Where it sits in the hierarchy

Ordered by distance - 1 is a direct parent or child.

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