OMOP Concept 4215114

Pachyonychia congenita syndrome

StandardConditionSNOMED39427000Disorder
Maps from
3
Descendants
2
Valid from
31 Jan 2002
Valid to
31 Dec 2099
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Source codes that map to this concept

3 source codes normalize to Pachyonychia congenita syndrome via the OMOP "Maps to" relationship.

VocabularyCodeNameType
CIEL131050Pachyonychia Congenita SyndromeNon-standard
MeSHD053549Pachyonychia CongenitaNon-standard
ReadPH55.00Congenital pachyonychiaNon-standard

Synonyms

Alternative names recorded for Pachyonychia congenita syndrome across source vocabularies.

  • Congenital pachyonychia
  • Jadassohn-Lewandowsky syndrome
  • Pachyonychia congenita
  • Pachyonychia congenita syndrome (disorder)
  • paquioniquia congénita
  • paquionixis congénita
  • síndrome de Jadassohn - Lewandowsky
  • síndrome de paquioniquia congénita
  • síndrome de paquioniquia congénita (trastorno)

Where it sits in the hierarchy

Ordered by distance - 1 is a direct parent or child.

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