OMOP Concept 36715141

Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome

StandardConditionSNOMED720639008Disorder
Maps from
1
Descendants
0
Valid from
31 Jan 2017
Valid to
31 Dec 2099
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Source codes that map to this concept

1 source code normalizes to Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome via the OMOP "Maps to" relationship.

VocabularyCodeNameType
MeSHC536729Zunich neuroectodermal syndromeNon-standard

Synonyms

Alternative names recorded for Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome across source vocabularies.

  • CHIME (coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability, ear anomaly) syndrome
  • CHIME syndrome
  • Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome (disorder)
  • Neuroectodermal dysplasia CHIME type
  • síndrome de coloboma, cardiopatía congénita, dermatosis ictiosiforme, discapacidad intelectual y anomalías auditivas
  • síndrome de coloboma, cardiopatía congénita, dermatosis ictiosiforme, discapacidad intelectual y anomalías auditivas (trastorno)
  • Zunich Kaye syndrome

Where it sits in the hierarchy

Ordered by distance - 1 is a direct parent or child.

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