OMOP Concept 194149

Congenital aganglionic megacolon

StandardConditionSNOMED204739008Disorder
Maps from
26
Descendants
14
Valid from
31 Jan 2002
Valid to
31 Dec 2099
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Source codes that map to this concept

26 source codes normalize to Congenital aganglionic megacolon via the OMOP "Maps to" relationship.

VocabularyCodeNameType
CIEL138604Hirschsprung's disease and allied congenital conditionsNon-standard
CIEL138605Hirschsprung's diseaseNon-standard
CIM10Q43.1Hirschsprung diseaseNon-standard
HPOHP_0002251Aganglionic megacolonNon-standard
ICD10Q43.1Hirschsprung diseaseNon-standard
ICD10CMQ43.1Hirschsprung's diseaseNon-standard
ICD10CNQ43.1Hirschsprung diseaseNon-standard
ICD10CNQ43.100Hirschsprung diseaseNon-standard
ICD10CNQ43.101Congenital short segment Hirschsprung (machine translation)Non-standard
ICD10CNQ43.102Congenital long segment Hirschsprung (machine translation)Non-standard
ICD10CNQ43.103Normal congenital megacolon (machine translation)Non-standard
ICD10CNQ43.104Congenital short segment Hirschsprung (machine translation)Non-standard
ICD10CNQ43.105Hirschsprung disease Source (machine translation)Non-standard
ICD10CNQ43.106Congenital colon Hirschsprung (machine translation)Non-standard
ICD10GMQ43.1Hirschsprung diseaseNon-standard
KCD7Q43.1Hirschsprung’s diseaseNon-standard
MeSHD006627Hirschsprung DiseaseNon-standard
Nebraska Lexicon204739008Congenital aganglionic megacolonNon-standard
Nebraska Lexicon268208007Hirschsprung disease and allied congenital conditionsNon-standard
ReadPB3..00Hirschsprung's disease and allied congenital conditionsNon-standard
ReadPB30.00Hirschsprung's diseaseNon-standard
ReadPB30z00Hirschsprung's disease NOSNon-standard
ReadPB31.00Idiopathic congenital megacolonNon-standard
ReadPB3..11AganglionosisNon-standard
ReadPB33.12Congenital aganglionic megacolonNon-standard
ReadPB3z.00Hirschsprung's disease and allied congenital conditions NOSNon-standard

Synonyms

Alternative names recorded for Congenital aganglionic megacolon across source vocabularies.

  • Aganglionic megacolon
  • aganglionosis
  • Aganglionosis
  • Congenital aganglionic megacolon (disorder)
  • enfermedad de Hirschsprung
  • HD - Hirschsprung's disease
  • Hirschsprung disease
  • Hirschsprung's disease
  • megacolon aganglionar
  • megacolon aganglionar congénito
  • megacolon aganglionar congénito (trastorno)

Where it sits in the hierarchy

Ordered by distance - 1 is a direct parent or child.

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